Congenital left ventricular aneurysm is a rare, poorly understood and potentially lethal congenital heart disease. Few pediatric cases have been reported. This aneurysm is defined as a fibrous outpouch with paradoxical contractility and appears to be a developmental anomaly, an idiopathic dysplasia of left ventricular endocardium and myocardium. We report a case of congenital left ventricular aneurysm presenting an abnormal electrocardiography in a 65-year old woman without cardiac symptoms. Congenital left ventricular aneurysm was diagnosed by echocardiography and left ventriculogram.