Hea Kyoung Yang; Ah Young Kim; Ryoung Kyoung Lim; Kyung Hee Park; Shin Yun Byun

doi:10.14734/kjp.2014.25.1.33

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Yang, Kim, Lim, Park, and Byun: A Case of Cantrell’s Syndrome with Left Ventricular Diverticulum in a Neonate

Original Article

Korean J Perinatol 2014;25(1):33-36.

Published online: 21 March 2014

DOI: https://doi.org/10.14734/kjp.2014.25.1.33

A Case of Cantrell’s Syndrome with Left Ventricular Diverticulum in a Neonate

Hea Kyoung Yang, M.D., Ah Young Kim, M.D., Ryoung Kyoung Lim, M.D., Kyung Hee Park, M.D., Shin Yun Byun, M.D.

Department of Pediatrics, Pusan National University School of Medicine, Yangsan, Korea

Received 9 January 201424 March 2014 Accepted 28 March 2014

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Cantrell's syndrome is a rare congenital anomaly, consists of five malformations. There are the midline abdominal wall defect, the defect of sterna lower part, an agenesis of the anterior part of the diaphragm, an absence of the diaphragmatic pericardium, and the congenital intracardiac problem. We diagnosed Cantrell’s syndrome with left ventricular diverticulum in a female neonate with no perinatal problems. She experienced an onestaged operation and discharged with no complications. We report a case with brief review of the literature.

Keywords: Cantrell’s, syndrome, Ventricular diverticulum, One-staged operation

REFERENCES

1.Cantrell JR., Haller JA., Ravitch MM. A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium, and heart. Surg Gynecol Obstet. 1958. 107:60214.

2.Angtuaco TL. Fetal anterior abdominal wall defect. In: Callen PW. editor. Ultrasonography in obstetrics and gynecology. 4th ed.Philadelphia: WB Saunders;2000. 157-9. p. 169–82.

3.Hertzberg BS., Nyberg DA., Neilsen IR. Ventral wall defects. In: Nyberg DA, McGahan JP, Pretorius DH, Pilu G. editors. Diagnostic imaging of fetal anomalies. Lippincott Williams & Wilkins;2003. p. 989–1000.

4.Seashore JH. Congenital abdominal wall defects. Clin Perinatol. 1978. 5:61–77.

5.Cha IW., Yoo MS., Park IS. A case of Cantrells pentalogy syndrome. Korean J Obstet Gynecol. 1983. 26:1073–6.

6.Cho HC., Chung IB., Choi SJ., Lee YH., Ha JW., Lee JJ. A case of Cantrell's pentalogy with anencephaly diagnosed by prenatal ultrasonography. Korean J Obstet Gynecol. 2004. 47:2490–3.

7.Sanchis Solera L., Beltra Pico R., Castro Sanchez M., Serrano Gonzalez A., Sanchez Lopez JM., Hernandez Navarro J, et al. Cantrell's pentalogy: Complete treatment, step by step. Cir Pediatr. 1992. 5:101–4.

8.Lowe JB., Williams JC., Robb D., Cole D. Congenital diverticulum of the left ventricle. Br Heart J. 1959. 21:101–6.

9.Orsmond GS., Joffe HS., Chesler E. Congenital diverticulum of the left ventricle associated with hypoplastic right ventricle and ventricular septal defect. Circulation. 1973. 48:1135–9.

10.Suehiro K., Okutani R., Ogawa S., Nakada K., Shimaoka H., Ueda M, et al. Perioperative management of a neonate with cantrell syndrome. J Anesth. 2009. 23:572–5.

11.Park JY., Kim SM., Park YH., Kim DJ., Yoo BW., Bang SO, et al. One-stage operation for Cantrell's pentalogy. J Korean Surg Soc. 2008. 75:282–4.

Fig. 1.

This image of the patient shows pulsating and protruding mass on the lower sternal area with abdominal wall defect to umbilicus.

Fig. 2.

The abdominal ultrasound shows a defect of abdominal wall (A, arrow) and umbilical hernia (B, arrow).

Fig. 3.

The Abdominal CT shows eventration of cardiac apex through dehiscent chest wall (A) and left ventricular diverticulum (B).

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