A Case of Idiopathic Infratentorial Superficial Siderosis

Daeun Shin; Seok-Yul Yang; Youngwook Kim; Ho-Sung Ryu; Hoseok Lee

doi:10.13104/imri.2020.24.1.51

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Shin, Yang, Kim, Ryu, and Lee: A Case of Idiopathic Infratentorial Superficial Siderosis

Case Report

iMRI 2020;24(1):51-54.

Published online: 19 January 2020

DOI: https://doi.org/10.13104/imri.2020.24.1.51

A Case of Idiopathic Infratentorial Superficial Siderosis

Daeun Shin¹, Seok-Yul Yang¹, Youngwook Kim¹, Ho-Sung Ryu¹, Hoseok Lee²

¹Department of Neurology, Kyungpook National University Hospital, Daegu, Korea

²Department of Radiology, Kyungpook National University Hospital, Daegu, Korea

Correspondence to: Ho-Sung Ryu, M.D. Department of Neurology, Kyungpook National University Hospital, 130, Dongduk-ro, Jung-gu, Daegu 41944, Korea. Tel. +82-53-200-5765 Fax. +82-53-422-4265 E-mail: ryuhosung138@gmail.com

Received 18 September 20195 November 2019 Accepted 11 November 2019

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Superficial siderosis is attributed to hemosiderin deposition in the subpial layers of the nervous system. The clinical features of infratentorial superficial siderosis (ISS) are hearing loss, cerebellar ataxia, and corticospinal tract signs and the most common cause of idiopathic ISS is a dural defect. As magnetic resonance imaging (MRI) has advanced, the diagnosis of infratentorial superficial siderosis can be confirmed by unique radiological findings in MRI. Here, we report on a female patient diagnosed with idiopathic ISS by means of clinical symptoms and radiological findings.

Keywords: Superficial siderosis, Hearing loss, Cerebellar ataxia

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Fig. 1.

Idiopathic infratentorial superficial siderosis. Brain magnetic resonance imaging (MRI) (a-c) and spine MRI (km) show low signal intensities in the cerebrum, cerebellum, brain stem, and spinal cord in T2-weighted images and the corresponding T2∗-weighted gradient-recalled echo (GRE) images (d-f) or susceptibility-weighted images (SWI) (g-i) show low signal intensities in the same regions, which suggest a typical hemosiderin deposition pattern. The “blooming” effect on the SWI (h, arrowhead) is more remarkable compared to that on the T2-weighted GRE images (e, asterisk). Spine MRI (j-m) shows cerebrospinal fluid collection (arrows).

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