A case of atresia of the esophagus, with no esophageal communication with the trachea, in a 3 days old babywas reported. As far as we know, this type could be seen in 3 to 7 percent of all cases of the esophageal atresia.In this case, the diagnosis was confirmed by esophagography with thin barium meal. Literatures are also reviewedbriefly.