A lymphangioma, which is analogous in some ways to hemangioma due to a common origin, develop and grow in identical fashion and show certain common features in response to treatment, is a benign tumor composed of lymphatic tissue. But lymphangiomas are much less common than hemangiomas in frequency and most of these lesions are usually present at birth. Most of these lesions are found in the neck, few are located in the axilla and the remainders are scattered throughout the body. Soft tissue hyertrophy of the thenar eminance and proximal portion of index finger of left hand due to congenital lymphangioma, 7-months male baby, treated by surgical resection is presented with a review of the literature.