Adenoid cystic carcinoma of the Bartholin's gland is a rare malignant tumor comprising less than 1% of all female genital tract tumors. Because of low incidence, knowledge of management and factors influencing the clinical outcome of patients is limited and there is no consensus regarding the most optimal treatment. We report a case of 73-year-old woman with adenoid cystic carcinoma of the Bartholin's gland.