Granulosa cell tumors of the ovary account for 2-5% of all ovarian malignancies but, nearly three-quarters of all sex-cord stromal tumors. Juvenile granulosa cell tumors differ from the adult type in regard to their clinical and pathological features and biological behavior. In premenarcheal girls, these tumors are associated with sexual precocity. About 90% are diagnosed in early stage (FIGO I) with a favorable prognosis. More advanced stages (FIGO II-IV) have a poor clinical outcome. We experienced a case of juvenile granulosa cell tumor and report it with a brief review of literatures.