A five-month-old female Shih-tzu puppy was presented for repair of congenital choristoma in left eye. The patient was suffered from chronic epiphora and ocular discharge during 3 months. On ophthalmic examination, left eye revealed hyperemia in conjunctiva of the temporal canthus due to choristoma with hair. At surgery, the choristoma invaded by stromal layer of the cornea, and extended to limbus and conjunctiva. Based on the anatomical location and histopathological features of the removed tissue, the choristoma was diagnosed as corneal dermoid.