A 34-year-old male complained of severe tenderness to light touch on the lateral aspect of the distal left arm for 4 months. Four years ago, he had a history of excisional biopsy for the same symptom at other hospital. Histopathologically, the diagnosis was made as a glomus tumor. And meticulous surgical excision resulted in complete cure of this tumor. We report this case because extramanual location of this tumor was relatively rare and recurrence of it after excision was very rare.