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Kang, Oh, Ko, Seo, Park, Kang, and Kim: A Case of Blue Rubber Bleb Nevus Syndrome
Case Report

Korean Journal of Pediatric Gastroenterology and Nutrition 2008; 11(2): 198-203.

Published online: 30 September 2008

DOI: https://doi.org/10.5223/kjpgn.2008.11.2.198

A Case of Blue Rubber Bleb Nevus Syndrome

Ki Soo Kang, Hyun Ju Oh, Jae Sung Ko*, Jeong Kee Seo*, Kwi Won Park†, Gyeong Hoon Kang‡, Woo Sun Kim§

Department of Pediatrics, Cheju National University College of Medicine, Jeju, Korea.

*Department of Pediatrics, Seoul National UniversityCollege of Medicine, Seoul, Korea.

†Department of Surgery, Seoul National UniversityCollege of Medicine, Seoul, Korea.

‡Department of Pathology, Seoul National UniversityCollege of Medicine, Seoul, Korea.

§Department of Radiology, Seoul National UniversityCollege of Medicine, Seoul, Korea.

jkseo@snu.ac.kr

Copyright © 2008 The Korean Society of Pediatric Gastroenterology, Hepatology and Nutrition

Abstract

We report a 10-year-old girl with the blue rubber bleb nevus syndrome (BRBNS) who had chronic severe anemia caused by chronic occult bleeding in the gastrointestinal (GI) tract. The patient was admitted to the hospital frequently for recurrent pallor and fatigue since the age of 7 years. Gastroduodenoscopy and capsule endoscopy revealed multiple venous malformations with blood oozing in the stomach, small bowel and colon. The patient was treated by aggressive surgical resection of the 23 vascular malformations in the GI tract. The patient is well without anemia 15 months post surgery.

Keywords: Blue rubber bleb nevus syndrome, Gastrointestinal bleeding, Vascular malformation

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