Flail arm syndrome with several issues related to the diagnostic process

Jae-Youn Kim; Yun Kyung Park; Bora Yoon; Kee Ook Lee; Yong-Duk Kim; Sang-Jun Na

doi:10.14253/acn.2017.19.1.68

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Kim, Park, Yoon, Lee, Kim, and Na: Flail arm syndrome with several issues related to the diagnostic process

Case Report

Ann Clin Neurophysiol 2017;19(1):68-70.

Published online: 5 January 2017

DOI: https://doi.org/10.14253/acn.2017.19.1.68

Flail arm syndrome with several issues related to the diagnostic process

Jae-Youn Kim, Yun Kyung Park, Bora Yoon, Kee Ook Lee, Yong-Duk Kim, Sang-Jun Na

Department of Neurology, Konyang University of College of Medicine, Daejeon, Korea

Correspondence to Sang-Jun Na Department of Neurology, Konyang University Hospital, Konyang University of College of Medicine, 158 Gwanjeodong-ro, Seo-gu, Daejeon 35365, Korea Tel: +82-42-600-8814 Fax: +82-42-545-0050 E-mail: nukedoc@hanmail.net

Received 2 September 201629 December 2016 Accepted 2 January 2017

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

초록

Flail arm syndrome (FAS), known as one of the atypical amyotrophic lateral sclerosis (ALS) variants, has a similar clinical course and pathologic findings as ALS. Therefore it is difficult to differentiate between ALS and FAS at a glance. There are few reports involving individual analysis of FAS patients to date. The findings of polysomnography (PSG) in patient with FAS are not well known. We report a male FAS patient with review of literatures and several issues related to the diagnostic process.

Keywords: Flail arm syndrome, Amyotrophic lateral sclerosis, Upper motor neuron sign

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