Journal List > J Korean Soc Hypertens > v.19(1) > 1089811

Park: Middle Aortic Syndrome with Superior Mesenteric and Bilateral Renal Artery Involvement: Unusual Type of Aortic Coarctation

ABSTRACT

Middle aortic syndrome (MAS) is very uncommon vascular pathology characterized by a long segmental narrowing or obstruction of the abdominal and/or distal thoracic aorta, commonly involving with the visceral and renal arteries. This syndrome may be presented with various physical signs of coarctation of the aorta, including resistant hypertension, renal insufficiency and/or mesenteric ischemia. Here, we report a case of a 64-year-old man with severe hypertension. He was diagnosed with MAS associated with stenosis of visceral and renal vessels by use of computed tomography and magnetic resonance angiography.

References

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Fig. 1.
Imaging of computed tomography (CT) and magnetic resonance angiography (MRA). (A) Origin of right renal artery (arrow) was not found around aorta, supplied by branch vessels arose from distal superior mesenteric artery and left renal artery. (B) Left renal artery (arrow) originating from hypoplastic abdominal aorta was severely calcified and stenosed. (C) Abrupt luminal obstruction of abdominal aorta just below the celiac trunk (Upper arrow). Superior mesenteric artery is supplied by the arc of Riolan (Lower arrow). Both iliac arteries are normal. (D) MRA showing similar but more detailed vasculature as compared with CT.
jksh-19-39f1.tif
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