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Kang, Kim, Park, Lim, Park, Park, and Jun: A case of Herlyn-Werner-Wunderlich syndrome diagnosed in asymptomatic newborn
Case Report
Korean Journal of Obstetrics & Gynecology

Korean Journal of Obstetrics & Gynecology 2012; 55(12): 966-969.

Published online: 18 December 2012

DOI: https://doi.org/10.5468/KJOG.2012.55.12.966

A case of Herlyn-Werner-Wunderlich syndrome diagnosed in asymptomatic newborn

Minji Kang, MD, Sung Woo Kim, MD, Jee Yoon Park, MD, Hae Jeng Lim, MD, Chan-Wook Park, MD, PhD, Joong Shin Park, MD, PhD, Jong Kwan Jun, MD, PhD

Department of Obstetrics and Gynecology, Seoul National University College of Medicine, Seoul, Korea.

Corresponding author: Joong Shin Park, MD, PhD. Department of Obstetrics and Gynecology, Seoul National University College of Medicine, 101 Daehak-ro, Jongno-gu, Seoul 110-744, Korea. Tel: +82-2-2072-3199, Fax: +82-2-762-3599, jsparkmd@snu.ac.kr

Received 31 May 2012       Revised 23 October 2012       Accepted 27 October 2012

Copyright © 2012. Korean Society of Obstetrics and Gynecology

(open-access):

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Herlyn-Werner-Wunderlich (HWW) syndrome is characterized by the triad of uterine didelphys, obstructed hemivagina, ipsilateral renal agenesis. Symptoms generally occur just after menarche about 12 to 13 years old and it is usually diagnosed by pelvis magnetic resonance imaging. It can be treated by marsupialization of obstructed hemivagina or vaginal septum resection. It can be complicated by infertility, endometriosis, pelvic cavity adhesion, pyosalpinx, pyocolpos, and recurrent miscarriage. Together with a brief review of literature, we report a case of HWW syndrome diagnosed in asymptomatic newborn who was suspected to have a genitourinary anomaly on prenatal ultrasonography.

Keywords: Herlyn-Werner-Wunderlich syndrome, Newborn, Asymptomatic

Figures and Tables

Fig. 1
Prenatal obstetric ultrasonographic view: suspicious for hydronephrosis grade III with right ectopic kidney with pelvocalyceal dilatation, dilated ureter, suspicious for ureterovesical junction obstruction or ureteropelvic junction obstruction.
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Fig. 2
Magnetic resonance imaging pelvis (non-contrast): there is no normal right kidney in renal fossa and uterine didelphys is detected.
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Fig. 3
Magnetic resonance imaging pelvis (non-contrast): there is an ectopic insertion of right ureter to urethra with marked dilatation of dysplastic pelvocalyceal system and ureter.
kjog-55-966-g003

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