Journal List > Korean J Obstet Gynecol > v.55(9) > 1088512

Korean J Obstet Gynecol. 2012 Sep;55(9):655-658. Korean.
Published online September 17, 2012.
Copyright © 2012. Korean Society of Obstetrics and Gynecology
Colon atresia, a rare comorbid condition in VACTERL association
Ji Hye Hwangbo, MD, Eun Young Heo, MD, Youn Sil Choo, MD, Jin Young Bae, MD, Mi Ju Kim, MD and Won Joon Seong, MD, PhD
Department of Obstetrics and Gynecology, Kyungbook National University School of Medicine, Deagu, Korea.

Corresponding author: Won Joon Seong, MD, PhD. Department of Obstetrics and Gynecology, Kyungbook National University School of Medicine, 130 Dongdeok-ro, Jung-gu,Deagu 700-721, Korea. Tel: +82-53-420-5724, Fax: +82-53-423-7905, Email:
Received May 03, 2012; Revised June 29, 2012; Accepted July 24, 2012.

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License ( which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.


Vertebral, anal, cardiac, tracheoesophageal, renal and limb (VACTERL) association is defined by the presence of at least three of the following six congenital malformations: vertebral defects, anal atresia, cardiac defects, tracheo-esophageal fistula, renal anomalies and limb abnormalities. The abdominal cystic mass, suspicious of colon atresia was identified on prenatal ultrasonography. The new born infant exhibited single umbilical artery, hemivertebra, hypoplastic nasal bone, ventricular septal defect, patent ductus arteriosus, colon atresia. For treatment of colon atresia, two staged surgery was provided by a pediatric surgeon. We experienced colon atresia, a very rare comorbid condition in VACTERL association. Prompt diagnosis and surgical correction was possible with the cooperation of pediatric surgeons, obstetricians and pediatricians.

Keywords: VACTERL association; Colon atresia; Congenital malformations


Fig. 1
At 28/6 weeks of gestation, the hemivertebra was identified between thoracic vertebra No.10 and No.11 on prenatal ultrosonogram (arrow).
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Fig. 2
At 38/1 weeks of gestation, the abdominal cystic mass 3×7 cm, suspicous of colon atresia was identified on ultrasonogram.
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Fig. 3
At 38/1 weeks of gestation, a left ectopic kidney was identified.
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Fig. 4
On the date of birth the baby showed a hypoplastic nasal bone (arrow).
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Fig. 5
On the first day of birth, the lopogram showed narrowing colon near the hepatic flexure, representing colon atresia (arrow).
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