Journal List > Korean J Obstet Gynecol > v.55(2) > 1088404

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Jeon, Kim, Chun, Cho, Ji, and Jeong: Pregnancy in woman with Klippel-Trenaunay syndrome: A case report
Case Report
Korean Journal of Obstetrics & Gynecology

Korean Journal of Obstetrics & Gynecology 2012; 55(2): 119-122.

Published online: 15 February 2012

DOI: https://doi.org/10.5468/KJOG.2012.55.2.119

Pregnancy in woman with Klippel-Trenaunay syndrome: A case report

Gyun-Ho Jeon, MD1, Yeon Mee Kim, MD2, Sungwook Chun, MD1, Hyun Jin Cho, MD1, Yong-Il Ji, MD1, Chul-Hoi Jeong, MD1

1Department of Obstetrics and Gynecology, Haeundae Paik Hospital, Inje University College of Medicine, Busan, Korea.

2Department of Pathology, Haeundae Paik Hospital, Inje University College of Medicine, Busan, Korea.

Corresponding author: Gyun-Ho Jeon, MD. Department of Obstetrics and Gynecology, Haeundae Paik Hospital, Inje University College of Medicine, 875 Haeun-daero, Haeundae-gu, Busan 612-862, Korea. Tel: +82-51-797-2020, Fax: +82-51-797-2030, jeon285@paik.ac.kr

Received 21 October 2011       Revised 9 December 2011       Accepted 9 January 2012

Copyright © 2012. Korean Society of Obstetrics and Gynecology

(open-access):

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

The Klippel-Trenaunay syndrome is rare congenital disease characterized by a triad of cutaneous vascular malformations, varicose veins, and hypertrophy of bone and soft tissue. Although several cases of pregnancy in women with Klippel-Trenaunay syndrome were reported as there may be increased risk of pregnancy- and/or delivery-associated complications such as varicosities, thromboembolism and hemorrhage, there is little general information regarding how to deal with pregnancy in patients with Klippel-Trenaunay syndrome and their obstetric outcome. We describe the case of a woman suffering from Klippel-Trenaunay syndrome delivering a healthy child with a brief review of concerned literature.

Keywords: Klippel-Trenaunay syndrome, Pregnancy, Complications

Figures and Tables

Fig. 1
The swollen and slightly enlarged right leg was seen at 7 weeks of pregnancy age. Cutaneous capillary hemangiomas and varicose veins were extended on the medial and dorsal side of the right leg.
kjog-55-119-g001
Fig. 2
Transvaginal sonography reveals a 27 × 15 mm sized subchorionic hemorrhage during 1st trimester of pregnancy without definite hemangiomas around uterus.
kjog-55-119-g002
Fig. 3
Fibrin thrombi in fetal chorionic vessels were found in the placental biopsy (H&E, ×100).
kjog-55-119-g003

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