Journal List > Korean J Obstet Gynecol > v.54(11) > 1088366

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Park, Lim, Kim, Kim, and Moon: A case of myxoid leiomyosarcoma of uterus occurring in a 5-year-old girl: A case report and literature review
Case Report
Korean Journal of Obstetrics & Gynecology

Korean Journal of Obstetrics & Gynecology 2011; 54(11): 712-716.

Published online: 23 November 2011

DOI: https://doi.org/10.5468/KJOG.2011.54.11.712

A case of myxoid leiomyosarcoma of uterus occurring in a 5-year-old girl: A case report and literature review

Seong Nam Park, MD1, Hyae Won Lim, MD1, Hoon Young Kim, MD1, Byoung Ryun Kim, MD1, Hyung Bae Moon, MD2

1Department of Obstetrics and Gynecology, Wonkwang University College of Medicine, Iksan, Korea.

2Department of Pathology, Wonkwang University College of Medicine, Iksan, Korea.

Corresponding author: Byoung Ryun Kim, MD. Departments of Obstetrics and Gynecology, Wonkwang University College of Medicine, 344-2 Sinyong-dong, Iksan 570-711, Korea. Tel: +82-63-859-1545, Fax: +82-63-852-7520, brkim21@lycos.co.kr

Received 28 July 2011       Revised 16 September 2011       Accepted 19 September 2011

Copyright © 2011. Korean Society of Obstetrics and Gynecology

(open-access):

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Myxoid leiomyosarcoma of the uterus is a variant of leiomyosarcoma characterized by a large amount of myxomatous stroma and low mitotic counts with minimal cellular atypia but with subsequent malignant course. These tumors have a striking myxoid appearance and exhibit highly malignant behavior despite their low mitotic index. We report a first case of myxoid leiomyosarcoma of the uterus occurring in a young child with brief review of literatures.

Keywords: Myxoid leiomyosarcoma, Uterus, A young child

Figures and Tables

Fig. 1
(A) Abdominopelvic computed tomographic scan after enhancement show 12.3 × 11.8 cm sized, heterogenous enhancing solid mass in abdominal cavity (M, mass; B, bladder). (B) The upper portion of the resected tumor showing gelatinous consistency (arrow).
kjog-54-712-g001
Fig. 2
The smooth muscle cells are widely separated by myxoid material & increased mitotic figures (arrow) (A, H&E, ×200; B, H&E, ×400).
kjog-54-712-g002
Fig. 3
(A) Immunohistochemical staining of smooth muscle cell actin (×400). (B) Immunohistochemical staining of vimentin (×400). (C) A large amount of myxoid matrix with cells forming an interanastomosing filigree pattern (alcian-blue, ×400).
kjog-54-712-g003

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