Journal List > Korean J Obstet Gynecol > v.54(5) > 1088282

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Jeon, You, Kwon, Yoon, Kang, Kim, Chae, Kim, and Kang: A case of the uterus didelphys with unilateral obstructed hemivagina and ipsilateral renal agenesis
Case Report
Korean Journal of Obstetrics & Gynecology

Korean Journal of Obstetrics & Gynecology 2011; 54(5): 273-277.

Published online: 25 May 2011

DOI: https://doi.org/10.5468/KJOG.2011.54.5.273

A case of the uterus didelphys with unilateral obstructed hemivagina and ipsilateral renal agenesis

Eun-Jin Jeon, MD, Rae-Mi You, MD, Su-Kyeong Kwon, MD, Jae-Won Yoon, MD, Huk-Jae Kang, MD, Sung-Hoon Kim, MD, Hee-Dong Chae, MD, Chung-Hoon Kim, MD, Byung-Moon Kang, MD

Department of Obstetrics and Gynecology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.

Corresponding author: Rae-Mi You, MD. Department of Obstetrics and Gynecology, Asan Medical Center, University of Ulsan College of Medicine, 388-1 Pungnap-dong, Songpa-gu, Seoul 138-736, Korea. Tel: +82-2-3010-1820, Fax: +82-2-3010-6944, ttadak@hanmail.net

Received 4 April 2011       Accepted 18 April 2011

Copyright © 2011. Korean Society of Obstetrics and Gynecology

(open-access):

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Uterus didelphys with unilateral obstructed hemivagina, and ipsilateral renal agenesis is a rare congenital anomaly due to Müllerian duct malformation. The most common clinical manifestation is dysmenorrhea, pelvic pain, vaginal or pelvic mass after menarche. Early diagnosis is important, to preserve fertility, to prevent adhesion due to retrograde menstruation, hematometra, hematosalpinx and endometriosis which lead to distorted pelvic anatomy. These anomalies could be diagnosed with ultrasonography and magnetic resonance imaging. Resection or incision of vaginal septum is adequate treatments to relieve symptoms and reserve fertility. We report a case of uterus didelphys with unilateral obstructed hemivagina and ipsilateral renal agenesis with a brief review of the literature.

Keywords: Uterus didelphys, Obstructed hemivagina, Ipsilateral renal agenesis

Figures and Tables

Fig. 1
Transvaginal ultrasonography shows a large paravaginal cystic mass, 4.5×3.5 cm with turbid content.
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Fig. 2
(A) MRI shows uterus didelphys. (B) MRI shows paravaginal cystic mass. (C) MRI shows absence of Lt kidney.
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Fig. 3
Laparoscopic finding shows uterus didelphys and normal finding of both ovaries and salpinges.
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Fig. 4
Diagram of resection of vaginal septum providing drainage of the retained pus.
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Fig. 5
After opertation, the paravaginal mass was disappeared in MRI.
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