Journal List > Korean J Leg Med > v.39(3) > 1087974

TOOLS
Ha, Park, and Cho: [secondary publication] Traumatic Rupture of a Huge Renal Angiomyolipoma in a Tuberous Sclerosis Patient
증 례

Korean J Leg Med 2015;39(3):84-87.

Published online: 17 January 2015

DOI: https://doi.org/10.7580/kjlm.2015.39.3.84

[secondary publication] Traumatic Rupture of a Huge Renal Angiomyolipoma in a Tuberous Sclerosis Patient

Hongil Ha1, Jong Hyeok Park1, Na-Young Cho2

1Division of Forensic Medicine, Busan Institute, National Forensic Service, Yangsan, Korea

2Busan Metropolitan Police Agency, Busan, Korea

Correspondence to Hongil Ha Division of Forensic Medicine, Busan Institute, National Forensic Service, 50 Geumoh-ro, Mulgeum-eup, Yangsan 626-742, Korea Tel: +82-55-380-4050 Fax: +82-55-380-4060 E-mail: sanchee@korea.kr

Received 20 January 2015       Revised 31 January 2015       Accepted 17 August 2015

Copyright © 2015 The Korean Society for Legal Medicine

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

A renal angiomyolipoma (AML) is an unusual benign tumor that is composed of adipose tissue, smooth muscle, and abnormal blood vessels. AMLs can occur sporadically or can be associated with tuberous sclerosis. A ruptured renal AML may manifest as lift-threatening hypovolemic shock or sudden death. Herein, the authors present an autopsy case of traumatic rupture of a renal AML in a patient with tuberous sclerosis.

Keywords: Angiomyolipoma, Tuberous sclerosis, Rupture, Autopsy

REFERENCES

1. Eble JN, Sauter G, Epstein JI, et al. Pathology and genetics of tumours of the urinary system and male genital organs. Lyon: IARC Press;2004. p. 65–7.
2. Louis DN, Ohgaki H, Wiestle OD, et al. WHO classification of tumours of the central nervous system. Lyon: IARC Press;2007. p. 218–21.
3. Eble JN. Angiomyolipoma of kidney. Semin Diagn Pathol. 1998; 15:21–40.
4. Roach ES, Gomez MR, Northrup H. Tuberous sclerosis complex consensus conference: revised clinical diagnostic criteria. J Child Neurol. 1998; 13:624–8.
crossref

Fig. 1.
The scene.
kjlm-39-84f1.tif
Fig. 2.
There are many grayish tan papules on the nose and cheeks in a butterfly distribution.
kjlm-39-84f2.tif
Fig. 3.
(A) A well circumscribed, yellowish gray and focally calcified tumor (1.5×1 cm) is located at the wall of lateral ventricle. (B) Histologically, the tumor is composed mainly of elongated tumor cells forming streams and occasional polygonal cells with abundant, glassy cytoplasm (H&E, ×200).
kjlm-39-84f3.tif
Fig. 4.
(A) A well-encapsulated mass with nodular appearance is seen in the upper pole of left kidney. The cut surface of the mass is mostly grayish yellow and firm, and shows extensive hemorrhage. (B) Histologically. the tumor is composed of adipose tissue, smooth muscle and vessels (H&E, ×100).
kjlm-39-84f4.tif
TOOLS
Similar articles