Journal List > J Korean Soc Radiol > v.75(1) > 1087713

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Kim, Lee, Koh, and Maeng: MR Imaging Findings of Supratentorial Meningeal Hemangioblastoma: A Case Report
Head and Neck Radiology
Case Report

Journal of the Korean Society of Radiology 2016; 75(1): 26-29.

Published online: 1 July 2016

DOI: https://doi.org/10.3348/jksr.2016.75.1.26

MR Imaging Findings of Supratentorial Meningeal Hemangioblastoma: A Case Report

Gi Hong Kim, MD1, Ho Kyu Lee, MD1, Myeong Ju Koh, MD1, Young Hee Maeng, MD2

1Department of Radiology, Jeju National University Hospital, Jeju, Korea.

2Department of Pathology, Jeju National University Hospital, Jeju, Korea.

Corresponding author: Ho Kyu Lee, MD. Department of Radiology, Jeju National University Hospital, 15 Aran 13-gil, Jeju 63241, Korea. Tel. 82-64-717-1371, Fax. 82-64-717-1372, hoklee33@gmail.com

Received 21 January 2016       Revised 17 February 2016       Accepted 5 March 2016

Copyright © 2016 The Korean Society of Radiology

(open-access):

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Hemangioblastomas account for 1.1–2.5% of intracranial neoplasms. These tumors most commonly occur in the cerebellum. A 77-year-old woman had a hemangioblastoma, which showed the supratentorial meningeal mass without any history of von Hippel-Lindau disease.

Keywords: Supratentorial Neoplasms, Hemangioblastoma

Figures and Tables

Fig. 1

A 77-year-old woman with supratentorial meningeal hemangioblastoma.

A, B. Axial T1-weighted and T2 FLAIR image show a 3.7 cm, well-defined cystic mass (arrow) in the left frontal convexity. The cystic mass shows hypo signal intensity on T1-weighted MR image and high signal intensity on T2 FLAIR image. The cystic mass exhibits a high signal intensity portion (arrowheads) suggesting hemorrhage, on T1-weighted and T2 FLAIR images.
C. Coronal T2-weighted image shows plaque-like mural nodule (arrowhead) of intermediate to high intensity signal.
D, E. Axial and coronal gadolinium-enhanced T1-weighted fat-suppressed MR image show a rim-like enhancement of the mass (arrows) and plaque-like enhancing mural nodule (arrowheads).
F. Coronal gadolinium-enhanced T1-weighted fat-suppressed MR image shows dural tail with adjacent plaque-like enhancing mural nodule (arrow).FLAIR = fluid attenuated inversion recovery
jksr-75-26-g001
Fig. 2

Microphotographs showing numerous thin-walled vessels (A: H&E, × 200) and large, vacuolated stromal cells (B: H&E, × 400). Immunohistochemistry, highlighting the stromal cells, which are positive for NSE (C: × 200) and negative for EMA. Vascular endothelial cells reactive with CD31 (D: × 200) highlighting the positive reaction of stromal cells. Positive for NSE, negative for EMA, and positive for vascular endothelial cells of CD31 are inconsistent with meningioma.

EMA = epithelial membrane antigen, H&E = hematoxylin and eosin, NSE = neuron specific enolase
jksr-75-26-g002

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