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Yoon and Kim: Unilateral Pulmonary Vein Atresia: A Case Report
Chest Radiology

Journal of the Korean Society of Radiology 2014; 70(1): 31-34.

Published online: 14 January 2014

DOI: https://doi.org/10.3348/jksr.2014.70.1.31

Unilateral Pulmonary Vein Atresia: A Case Report

So Hwa Yoon, MD, Ki Jun Kim, MD

Department of Radiology, Incheon St. Mary's Hospital, The Catholic University of Korea College of Medicine, Incheon, Korea.

Corresponding author: Ki Jun Kim, MD. Department of Radiology, Incheon St. Mary's Hospital, College of Medicine, The Catholic University of Korea, 56 Dongsu-ro, Bupyeong-gu, Incheon 403-720, Korea. Tel. 82-32-280-5231, Fax. 82-32-280-5230, kjrad@catholic.ac.kr

Received 14 August 2013       Accepted 25 October 2013

Copyright © 2014 The Korean Society of Radiology

(open-access):

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Unilateral pulmonary vein atresia is a rare congenital anomaly. Its symptoms begin to manifest in childhood and a broad spectrum of clinical severity has been described, ranging from asymptomatic, recurrent pulmonary infection, severe hemoptysis, to death. Only a few adult cases with this condition, with no or mild symptoms, have been reported. Pulmonary angiography has been typically used for definite diagnosis. However, pulmonary angiography may be replaced with the current developing multidetector CT. This report presents an adult case with mild symptoms, diagnosed by multidetector CT.

Keywords: Unilateral Pulmonary Vein Atresia, Multidetector Computed Tomography

Figures and Tables

Fig. 1
Rt. pulmonary vein atresia in 16-year-old man. Chest radiograph shows a small right hemithorax and diminished vessel size in the right lung with slight mediastinal displacement to the right.
jksr-70-31-g001
Fig. 2
Rt. pulmonary vein atresia in 16-year-old man.
A. Axial CT scan (lung window) shows small right hemithorax with mild interlobular septal thickening in right lower lobe and right middle lobe.
B. Contrast-enhanced axial CT scan (mediastinal window) shows the small right pulmonary artery and normal left pulmonary artery.
C, D. Axial and coronal CT scan shows smooth margin of the left atrium with no pulmonary vein (thin arrows) and numerous dilated vessels seen on paraesophageal area, representing bronchial collaterals (thick arrow).
jksr-70-31-g002
Fig. 3
Rt. pulmonary vein atresia in 16-year-old man. Volume-rendered CT angiogram shows the diminutive right pulmonary artery.
jksr-70-31-g003

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