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Kim: Cervical Spinal Monostotic Fibrous Dysplasia: A Case Report
Musculoskeletal Radiology

Journal of the Korean Society of Radiology 2013; 69(3): 239-242.

Published online: 11 September 2013

DOI: https://doi.org/10.3348/jksr.2013.69.3.239

Cervical Spinal Monostotic Fibrous Dysplasia: A Case Report

Ok Hwa Kim, MD

Department of Radiology, Haeundae Paik Hospital, Inje University College of Medicine, Busan, Korea.

Corresponding author: Ok Hwa Kim, MD. Department of Radiology, Inje University Haeundae Paik Hospital, 875 Haeundae-ro, Haeundae-gu, Busan 612-896, Korea. Tel. 82-51-797-0380, Fax. 82-51-797-0325, okkimmd@hanafos.com

Received 13 May 2013       Accepted 26 June 2013

Copyright © 2013 The Korean Society of Radiology

(open-access):

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Monostotic fibrous dysplasia of the cervical vertebra is quite unusual. The author reports a case of monostotic fibrous dysplasia affecting the second cervical vertebra with descriptions from the CT, MR and bone scanning findings.

Keywords: Fibrous Dysplasia, Monostotic, Spine, Computed Tomography, Magnetic Resonance Imaging

Figures and Tables

Fig. 1
Monostotic fibrous dysplasia of the C2 in a 42-year-old woman.
A, B. Coronal (A) and sagittal (B) CT scan of C-spine reveal the irregular margined osteolytic lesion with peripheral bony sclerosis, without evidence of the bony cortical destructions, in C2 body.
C-E. Sagittal MRI reveal the irregular margined osseous lesion incompletely surrounded by the rim of low signal intensity in the C2 body (arrows in C, D), showing low to intermediate SI on T1WI (C), heterogeneous mixed, low to high, SI on STIR image (D), and marked contrast enhancements (arrows in E) on Gd-T1WI (E) at the sites corresponding to the osteolytic areas of CT scan.
F. Bone scan following administration of Tc-99m MDP reveal the focal tracer uptake in the upper cervical spine. Note no other skeletal tracer uptake in the whole body scan.
G. Photomicrograph of surgical specimen shows classic microscopic appearance of fibrous dysplasia consisting of irregular immature trabeculae of woven bone with lack of osteoblastic rimming (arrowheads) in bland fibroblastic and collagenous matrix (arrows) (H&E stain, × 40).
Note.-Gd = gadolineum, MDP = methylene diphosphonate, SI = signal intensity, STIR = short tau inversion recovery, T1WI = T1-weighted image
jksr-69-239-g001

References

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