Journal List > Endocrinol Metab > v.25(3) > 1085835

Kwak, Kim, Seo, Jang, Park, and Kim: A Case of Pheochromocytoma Presented with Cardiogenic Shock and Followed by Spontaneous Remission

Abstract

Pheochromocytoma is derived from the chromaffin cells and patients with pheochromocytoma present with several signs and symptoms by producing, storing and secreting catecholamine. Spontaneous rupture or necrosis of pheochromocytoma is extremely rare, but it can be lethal because of the dramatic change in the circulation such as an acute abdominal emergency or shock. Spontaneous remission of the clinical symptoms due to necrosis of the pheochromocytoma is rare. We describe such a case that presented with cardiogenic shock due to extensive necrosis of the pheochromocytoma and this was followed by spontaneous remission of the clinical symptoms without removal of the pheochromocytoma.

Figures and Tables

Fig. 1
A. Abdominal computed tomography shows about 4 × 4 cm sized, relatively well-defined low density mass lesion with peripheral wall enhancement (arrow) in the left adrenal gland. B. After three months, the size of relatively well-defined low density mass lesion with peripheral wall subtle enhancement (about 1.5 × 1.5 cm) is decreased (arrow).
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Fig. 2
131I-MIBG scan shows no demonstrable abnormal finding.
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