The Abnormalities in Neuro-Imaging and Somatosensory Evoked Potentials in Hirayama Disease

Jin-Sung Park; Sang-Hoon Lee

doi:10.14253/KJCN.2015.17.1.38

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Park and Lee: The Abnormalities in Neuro-Imaging and Somatosensory Evoked Potentials in Hirayama Disease

Original Article

Korean J Community Nutr 2015;17(1):38-40.

Published online: 18 December 2015

DOI: https://doi.org/10.14253/KJCN.2015.17.1.38

The Abnormalities in Neuro-Imaging and Somatosensory Evoked Potentials in Hirayama Disease

Jin-Sung Park¹, Sang-Hoon Lee²

¹Department of Neurology, Kyungpook National University School of Medicine, Daegu, Korea

²Department of Radiology, Kyungpook National University Medical Center, Daegu, Korea

Address for correspondence; Jin-Sung Park Department of Neurology, Kyungpook National University Hospital, 680 Gukchaebosang-ro, Jung-gu, Daegu 700-842, Korea Tel: +82-53-200-2753 Fax: +82-53-200-2168 E-mail: jinforeva@gmail.com

Received 12 November 2014 Revised 6 February 2015 Accepted 26 February 2015

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Keywords: Hirayama disease, Magnetic resonance imaging, Evoked potentials

REFERENCES

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2.Zhou B., Chen L., Fan D., Zhou D. Clinical features of Hirayama disease in mainland China. Amyotroph Lateral Scler. 2010. 11:133–139.

3.Sonwalkar HA., Shah RS., Khan FK., Gupta AK., Bodhey NK., Vottath S, et al. Imaging features in Hirayama disease. Neurol India. 2008. 56:22–26.

4.Hassan KM., Sahni H., Jha A. Clinical and radiological profile of hirayama disease: a flexion myelopathy due to tight cervical dural canal amenable to collar therapy. Ann Indian Acad Neurol. 2012. 15:106–112.

5.Yin B., Liu L., Geng DY. Features of Hirayama disease on fully flexed position cervical MRI. J Int Med Res. 2011. 39:222–228.

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7.Wang XN., Cui LY., Liu MS., Guan YZ., Li BH., DU H. A Clinical neurophysiology study of Hirayama disease. Chin Med J (Engl). 2012. 125:1115–1120.

Fig. 1.

Cervical magnetic resonance imaging (MRI) and right median somatosensory evoked potentials (SEP) of the patient. The T2 weighted MRI with neck in neutral position was unremarkable while T2 weighted MRI with neck in flexion shows anterior displacement of the posterior dural sac (A, B). The reversible inter-peak latency between N13 and N19 on supine (5.5 ms) (C) and flexed (7.45 ms) (D) somatosensory evoked potentials (SEP) in the symptomatic side also support the diagnosis of Hirayama disease. (Normal SEP interpeak latency < 6.59 ms).

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