A Fatal Case of Full-Blown Neuro-Behcet Disease

Boo Suk Na; Young Nam Kwon; Soo Jin Song; Jong Min Song; Ho Geol Woo; Dokyung Lee; Tae-Beom Ahn

doi:10.14253/KJCN.2015.17.1.28

Journal List > Korean J Clin Neurophysiol > v.17(1) > 1084154

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Na, Kwon, Song, Song, Woo, Lee, and Ahn: A Fatal Case of Full-Blown Neuro-Behcet Disease

Original Article

Korean J Community Nutr 2015;17(1):28-30.

Published online: 18 December 2015

DOI: https://doi.org/10.14253/KJCN.2015.17.1.28

A Fatal Case of Full-Blown Neuro-Behcet Disease

Boo Suk Na, Young Nam Kwon, Soo Jin Song, Jong Min Song, Ho Geol Woo, Dokyung Lee, Tae-Beom Ahn

Department of Neurology, College of Medicine, Kyung Hee University, Seoul, Korea

Address for correspondence; Tae-Beom Ahn Department of Neurology, Kyung Hee University Hospital, 23 Kyungheedae-ro, Dongdaemun-gu, Seoul 130-872, Korea Tel: +82-2-958-8448 Fax: +82-2-958-8490 E-mail: ricash@hanmail.net

Received 21 October 2014 Revised 20 February 2015 Accepted 20 April 2015

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

We reported a 48-year-old man with Behcet disease, who presented with right hemiparesis. His first brain MRI showed multiple enhanced lesions. During the recovery, he had an episode of left 6th nerve palsy without new lesions in a follow-up MRI. Third episode was cervical myelitis, resulting in respiratory difficulty and quadriplegia without any reflexes. The myelitis was not responsive to immunotherapy. He died of respiratory failure complicated with pneumonia. This is a rare case of full-blown neuro-Behcet disease. (Korean J Clin Neurophysiol 2015;17:28-30)

Keywords: Behcet disease, Neuro-Behcet disease, Brainstem, Spinal cord

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Fig. 1.

Brain magnetic resonance imaging (MRI) shows multiple lesions in the left pons and the temporooccipital cortices on gadolinium (Gd)-enhanced T1 weighted images. Tentorium cerebelli are also enhanced by Gd (A). Spine MRI shows high signal intensity on T2 weighted image in the cervical cord (B).

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