Osteopetrosis is a rare skeletal disorder characterized by increased bone radiodensity with diminished bone resorption due to malfunction of the osteoclasts. Orthopaedic problems in the intermediate and autosomal dominant form include increased fracture, coxa vara, long bone bowing, hip and knee degenerative arthritis, and mandibular and long bone osteomyelitis. Healing of osteopetrotic bone is slow, and surgical treatment may be complicated by unusual technical problems of internal fixation due to bony hardness. The authors have experienced three cases of fracture with osteopetrosis and those cases are to be reported with exhaustive review of reference.