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Kim, Cho, Lee, Kim, Ryu, Park, Oh, Park, Choi, Seo, and Lee: Ebstein's Anomaly in Adults
Original Article
Korean Circulation Journal

Korean Circulation Journal 1988; 18(4): 673-680.

Published online: 31 December 1988

DOI: https://doi.org/10.4070/kcj.1988.18.4.673

Ebstein's Anomaly in Adults

Myung A Kim, M.D., Seoung Wook Cho, M.D., Woo Seung Lee, M.D., Dong Un Kim, M.D., Kyu Hyung Ryu, M.D., Seong Wook Park, M.D., Byung Hee Oh, M.D., Young Bae Park, M.D., Yun Shik Choi, M.D., Jung Don Seo, M.D., Young Woo Lee, M.D.

Copyright © 1988 The Korean Society of Circulation

(open-access):

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Clinical features, laboratory and operative findings were reviewed in 17 cases adult Ebstein's anomaly admitted to Seoul National University Hospital from Feburary,1979 to October, 1987.
1) Mean age of first diagnosis was 28.6 tears old(range ; 14-57 years old).
2) Exertional duspnea(88.2%) and palpitation(64.7%) were the predominant symptoms, and PSVT was documented in 4 cases among 11 patoents with palpitation.
3) Echocardiogram showed displacement or delayed closure of the tricuspid valve in 13 cases.
4) On similtaneous recording of the intracardiac ECG and pressure, right ventricular electrogram with atrial pressure in atrialized right ventricle was observed in all cases.
5) Right ventriculogram revealed displacement of the tricuspid valve in 9 cases and tricuspid regurgitation in 10 cases.
6) Interatrial communication via ASD(8) and PFO(3) was present in 11 cases(64.7%).
7) Operative finding of 9 cases showed abnormalities of septal leaflet in 9(100%), posterior leaflet in 8(88.8%), and anterior leaflet in 2 cases(22.2%).

Keywords: Ebstein's anomaly

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