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Lee, Han, Youn, and Kim: A Case Report of Gardner-Associated Fibroma in 19-Month-Old Girl
Case Report

Journal of the Korean Association of Pediatric Surgeons 2017; 23(2): 59-61.

Published online: 20 December 2017

DOI: https://doi.org/10.13029/jkaps.2017.23.2.59

A Case Report of Gardner-Associated Fibroma in 19-Month-Old Girl

Ho Lee, Ji-Won Han, Joong Kee Youn, Hyun-Young Kim

Department of Pediatric Surgery, Seoul National University Children's Hospital, Seoul, Korea.

Correspondence: Hyun-Young Kim, Department of Pediatric Surgery, Seoul National University Children's Hospital, 101 Daehak-ro, Jongno-gu, Seoul 03080, Korea. Tel: +82-2-2072-2478, Fax: +82-2-747-5130, spkhy02@snu.ac.kr

Received 7 April 2017       Revised 5 June 2017       Accepted 21 June 2017

Copyright © 2017 Korean Association of Pediatric Surgeons

Korean Association of Pediatric Surgeons

(open-access):

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Gardner-associated fibroma (GAF) is a benign lesion of soft tissue which has recently been described and is exceedingly rare in children. GAF is associated with adenomatous polyposis coli gene mutation, familial adenomatous polyposis and desmoid. We report a case of patient with soft tissue tumor on her lower back which was turned out to be GAF. The patient was a 19-month-old female who visited out-patient clinic with palpable mass on her lower back and we performed surgical excision. The tumor was located at subcutaneous and we excised the tumor including surrounding soft tissue. She discharged without any complication on surgery day. The pathologic report showed dense collagenous tissue with spindle cell and adipose tissue, suggestive of GAF. We are planning to check gene study and to perform endoscopy and abdominal ultrasonography for at the age of 4.

Keywords: Gardner syndrome, Fibroma, Adenomatous polyposis coli, Children

Figures and Tables

Fig. 1

Ultrasound finding of lesion (arrows).

jkaps-23-59-g001
Fig. 2

Gross picture of specimen; the specimen was divided into several pieces and the size of biggest one was 1.5×1.3×0.4 cm.

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Fig. 3

Microscopic finding of specimen; dense collagenous tissue with balnd spindle cells and adipose tissue (H&E, ×40).

jkaps-23-59-g003

Notes

CONFLICTS OF INTEREST No potential conflict of interest relevant to this article was reported.

References

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