Proteus syndrome is a rare congenital hamartomatous condition with a variety of abnormalities affecting allthree germ layers including overgrowth of various parts of the body, hemihypertrophy, unusual skeletalmalformation, skin lesions, and various tumors. I describe the radiologic findings in a 12 year-old boy withProteus syndrome. Computed tomography and magnetic resonance imaging are very useful for the specific diagnosis.