Uterine Didelphys with Blind Hemivagina, Hematocolpos, Ipsilateral Renal Agenesis (UD-BHRA) and Bilateral Ovarian Tumors : A Case Report1

Young Rae Lee; Byung Ik Choi; Hae Won Park; Shin Ho Kook

doi:10.3348/jkrs.1998.38.3.519

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Lee, Choi, Park, and Kook: Uterine Didelphys with Blind Hemivagina, Hematocolpos, Ipsilateral Renal Agenesis (UD-BHRA) and Bilateral Ovarian Tumors : A Case Report1

A Case Report

J Korean Radiol Soc 1998;38(3):519-522.

Published online: 18 December 1998

DOI: https://doi.org/10.3348/jkrs.1998.38.3.519

Uterine Didelphys with Blind Hemivagina, Hematocolpos, Ipsilateral Renal Agenesis (UD-BHRA) and Bilateral Ovarian Tumors : A Case Report¹

Young Rae Lee, M.D., Byung Ik Choi, M.D.², Hae Won Park, M.D., Shin Ho Kook, M.D.

¹Department of Radiology, Sungkyunkwan University, Kangbuk Samsung Hospital

²Department of Obstetrics & Gynecology, Sungkyunkwan University, Kangbuk Samsung Hospital

Address reprint requests to: Young Rae Lee, M.D., Department of Radiology, Kangbuk Samsung Hospital, « 108 Pyung-Dong, Jongno Ku, Seoul, 110-634, Korea. Tel. 82-2-739-3211 Fax. 82-2-738-1369

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Uterine didelphys is a congenital malformation characterized by the presence of two separated hemiuteri and hemivaginas, due to lack of midfusion of the Mullerian ducts. We report a case of UD-BHRA(uterine didelphys with blind hemivagina and ipsilateral renal agenesis), a rare type of uterine didelphys charaterized by symptomatic unilateral hematocolpos due to blind hemivagina after menarche and ipsilateral renal agenesis. The MRI findings in 22-year-old woman with bilateral ovarian tumors demonstrated two separated uterine horns and cervical and vaginal canals, with left hematocolpos and left renal agenesis.

Keywords: Uterus, MR, Uterus, abnormalities Ovary, neoplasms

REFERENCES

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Fig. 1.

A case of uterine didelphys with blind hemivagina and ipsilateral renal agenesis in 22-year-old female. A. SE Tl weighted (TR/TE=600/h) axial scan shows left renal agenesis. B. FSE T2 weighted (TR/TE=3000/85) axial scan shows two separated uterine cavities with normal signal intensities of the endometrium and the junctional zones(arrows). C. FSE T2 weighted (TR/TE=4000/85) sagittal image shows high signal intensity of paravaginal mass representing hematocolpos (arrows) and the right ovarian tumor (arrowheads) proved as yolk sac tumor mixed with teratoma. D SE Tl weighted (TR/TE=600/ll) axial scan shows intermediate signal intensitiy of right ovarian mass (arrows) and high signal intensity of left ovarian mass (arrow heads) proved as mature teratoma. E- F. FSE T2 weighted (TR/TE=3000/85) axial images peroformed after operation clearly demonstrated two separated uterocervical canals (arrows on Fig. E)and hemivaginas (arrows on Fig. F) without communication.

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