Journal List > J Rheum Dis > v.22(6) > 1064228

Yoo, Hwang, and Ahn: A Case of Relapsing Polychondritis Presenting with Diffuse Tracheobronchial Involvement

Abstract

Relapsing polychondritis is a rare autoimmune disease involving the cartilaginous structures of the whole body. Its diagnosis can be difficult when the typical clinical features such as auricular chondritis are absent. Here, we report on a case of a 51-year-old female who presented with cough, dyspnea, and polyarthritis. Chest computed tomography showed the diffuse involvement of tracheobronchial cartilage. According to Damiani's criteria, she was diagnosed as relapsing polychondritis even though there was no unique involvement of auricular cartilage, and high dose steroid and immunosuppressive therapy were then started. This case indicated that patients who have tracheobronchial cartilage involvement without definite auricular chondritis should be considered for relapsing polychondritis as a differential diagnosis.

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Figure 1.
Saddle nose deformity.
jrd-22-374f1.tif
Figure 2.
Chest computed tomography showed diffuse thickening of tracheobronchial wall (A) axial view (B) coronal view.
jrd-22-374f2.tif
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