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Abstract
Henoch-Schönlein purpura (HSP) is a systemic vasculitis involving the skin, gut, joint and kidney that is characterized by immunoglobulin A (IgA)-dominant immune de-posits in target organs. Gastrointestinal involvement is known to be relatively common, but acute pancreatitis and pulmonary involvement are rare in Henoch-Schönlein purpura. We experienced a case of a 46-year-old man who developed adult-onset HSP complicated by acute pancreatitis and interstitial pneumonitis. The patient received cortico-steroid therapy at a dosage of 0.5 mg/kg. After cortico-steroid therapy, patient's symptoms improved. We report here the first case of HSP complicated by acute pancreatitis and interstitial pneumonitis.
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Figure 1.
(A) Chest X-ray shows consolidation in the left upper lobe (LUL) on admission (arrow). (B) Chest CT shows focal ground- glass opacity in the LUL (arrow).
Figure 2.
(A) Abdomen CT shows diffuse and multi-loculated wall thickening of the small bowel (espe-cially the terminal ileum and ileum), on the first hospital day. (B) Abdomen CT shows fluid-filled bowel loops without wall thickening of the small bowel, on the third hospital day. (C) Abdomen CT shows diffuse wall thickening of the small bowel with fluid-filled bowel loops, on the seventh hospital day. (D) Colo-noscopy shows diffuse hyperemic edematous mucosa and erosions in the terminal ileum.
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