Journal List > Allergy Asthma Respir Dis > v.4(1) > 1059233

Kim, Son, and Park: Diffuse panbronchiolitis in an adolescent female

Abstract

Diffuse panbronchiolitis (DPB) is a progressive inflammatory respiratory disease of unknown cause mainly occurring in East Asian people. Studies on causes of the disease point to a genetic predisposition unique to Asians, but the cause remains unknown. If untreated, DPB progresses to bronchiectasis, respiratory failure, and death. The age of patients at onset of the disease varies from young to elderly people with a peak at 40–60 years. A few cases of DPB have been reported in Korean adults since 1992; however, the case of DPB in children is uncommon. Herein, we describe a 16-year-old girl with DPB who presented with chronic cough and sputum.

Figures and Tables

Fig. 1

Serial change of chest x-ray (A) in 2009; 4 years before diagnosis (B) in 2013; at initial diagnosis (C) in 2014; before treatment (D) in 2015; a year after treatment.

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Fig. 2

Chest computed tomography at initial diagnosis (A, B) and before treatment (C, D).

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