We report herein a rare and grotesque case of a 19-year-old male with faun tail on the lumbosacral area of the back, presented from birth. The lesion was a 10 × loan sized patch with the circumscribed tuft of coarse terminal hairs about 10 to 25 an in length downward like a horse-tail. In the center of the patch was a 4 × 3cm sized brown macule in which was a 2 × lan scar. The skin biopsy from the brown macule revealed mild hyperkeratosis with basilar hyperpigmentation. Lumbar radiography showed findings of spina bifida occulta affected from L-4 to total sacral segments. There was mild saddle-hypoesthesia in the neurologic study.