Woolly hair is the presence of Negroid hair on the scalp of non-Negroid people. We report a rare case of woolly hair on a 14-year-old Korean girl who presented with tightly-curled, fine and light brown hair which she had had since birth. Light microscopy disclosed flattening of the hair shafts with partial twists at irregular intervals. On scanning electron microscopy, the patient's hair revealed weathered cuticles, and twisted and flattened hair shafts.