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Kim, Park, Yoo, Kim, and Park: Three Cases of Congenital Smooth Muscle Hamartomas
Case Report

Annals of Dermatology 2007; 19(1): 38-42.

Published online: 31 March 2007

DOI: https://doi.org/10.5021/ad.2007.19.1.38

Three Cases of Congenital Smooth Muscle Hamartomas

Jung Keun Kim, M.D., Tae Ho Park, M.D., Jae Hak Yoo, M.D., Kea Jeung Kim, M.D., Hyang Joon Park, M.D.*

Department of Dermatology, Kangbuk Samsung Hospital, School of Medicine, Sungkyunkwan University, Seoul, Korea.

*Department of Dermatology, Cheil General Hospital, School of Medicine, Sungkyunkwan University, Seoul, Korea.

Corresponding author (chaptainkim@hanmail.net)

Copyright © 2007 The Korean Dermatological Association and The Korean Society for Investigative Dermatology

Abstract

Congenital smooth muscle hamartomas (CSMHs) usually appear at birth as skin-colored or slightly hyperpigmented patches or plaques on the trunk or extremities and are often covered by and increased amount of vellus hair. Histopathologically, it represents a proliferation of smooth muscle bundles within the dermis(1,2).
We herein report on three cases of localized CSMHs; Case 1 was a 2-month-old boy who presented with a skin-colored, 6×5 cm-sized plaque with folds, hypertrichosis and pseudo-Darier's sign on the face, an unusual site. But there was no hyperpigmentation. Case 2 and 3 were both 1-month-old boys who presented with typical hyperpigmented, hairy plaques on the lateral aspect of the left thigh.

Keywords: Congenital smooth muscle hamartoma, Hypertrichosis, Pseudo-Darier's sign

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