Journal List > J Korean Assoc Pediatr Surg > v.19(2) > 1015926

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Park and Park: Laparoscopic-Assisted Transanal Endorectal Pull-Through for Segmental Dilatation of Rectosigmoid Colon in a Child
Case Report

Journal of the Korean Association of Pediatric Surgeons 2013; 19(2): 156-161.

Published online: 24 December 2013

DOI: https://doi.org/10.13029/jkaps.2013.19.2.156

Laparoscopic-Assisted Transanal Endorectal Pull-Through for Segmental Dilatation of Rectosigmoid Colon in a Child

Ji young Park, M.D.1, Jinyoung Park, M.D.

1Department of Pathology, Graduate school of Medicine, Kyungpook National University, Taegu, Korea.

Department of Pediatric Surgery, Graduate school of Medicine, Kyungpook National University, Taegu, Korea.

Correspondence: Jinyoung Park, M.D., Department of Surgery, Kyungpook National University Hospital, 50 Samduk-2 Ga, Chung-gu, Taegu 700-721, Korea. Tel: 053)420-5612, Fax: 053)421-0510, kpnugs@knu.ac.kr

Received 16 October 2013       Accepted 29 November 2013

Copyright © 2013 Korean Association of Pediatric Surgeons

Abstract

Congenital segmental dilatation of the colon is a very rare entity of unknown etiology, characterized by a localized dilatation of a bowel segment of the colon of variable length and an abrupt transition between the normal and dilated intestine. It can affect any part of the colon, with the rectosigmoid colon being the most commonly affected site. The clinical and radiological features may resemble that of Hirschsprung disease, but differ in that the normal ganglion cells are found in the dilated and normal segment of the colon. We performed laparoscopic-assisted transanal endorectal pull-through for segmental dilatation of rectosigmoid colon in an 8-year-old boy with chronic constipation since the age of 5 months.

Keywords: Segmental dilatation, Rectosigmoid, Child

Figures and Tables

Fig. 1
Barium enema shows dilated rectosigmoid colon with abrupt transition to a normal proximal colon.
jkaps-19-156-g001
Fig. 2
Intraoperative photograph shows a localized dilatation of the rectosigmoid colon with normal colon proximally. Note also the dilated and tortuous mesocolic and serosal blood vessels.
jkaps-19-156-g002
Fig. 3
Microscopic examination shows marked hypertrophy of the inner circular muscle layer and abnormal location of ganglion cells (oblique arrows) within the inner circular muscle layer (H & E, × 20).
jkaps-19-156-g003

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