Journal List > Korean J Perinatol > v.24(4) > 1013696

Choi, Cho, Na, Kim, and Lim: Lumbocostovertebral Syndrome with Congenital Bilateral Lumbar Hernia

Abstract

Lumbocostovertebral syndrome is a rare type of congenital lumbar hernia. Its features include lumbar hernia associated with genitourinary, vertebral, and rib anomalies. About 30 cases have been reported in the English literature, but in Korea, there has not been a case reported. We experienced a neonate with multiple costovertebral anomalies and bilateral lumbar hernia with liver and small intestine herniation diagnosed by physical examination and computed tomography. We report a case of a congenital lumbocostovertebral syndrome in neonate with literature review.

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Fig. 1
Burging mass at the both flank area.
kjp-24-306f1.tif
Fig. 2
Chest X-ray show lumbar hernia and T9-T12 hemivertebrae, laterlization and caudalization of both lower rib.
kjp-24-306f2.tif
Fig. 3
Abdomen CT showing bilateral oblique muscle defect with herniation of liver and bowel.
kjp-24-306f3.tif
Fig. 4
Abdomen CT showing urachus.
kjp-24-306f4.tif
Fig. 5
Chest CT showinghemivertebrae on T9-T12.
kjp-24-306f5.tif
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