Coxa Vara with Spondylometaphyseal Dysplasia

Tai-Seung Kim; Suk-Hwan Kim; Kyu-Sung Chung

doi:10.4055/jkoa.2011.46.3.268

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Kim, Kim, and Chung: Coxa Vara with Spondylometaphyseal Dysplasia

Case Report

Journal of the Korean Orthopaedic Association

Journal of the Korean Orthopaedic Association 2011; 46(3): 268-272.

Published online: 30 June 2011

DOI: https://doi.org/10.4055/jkoa.2011.46.3.268

Coxa Vara with Spondylometaphyseal Dysplasia

Tai-Seung Kim, M.D., Suk-Hwan Kim, M.D., Kyu-Sung Chung, M.D.

Department of Orthopedic Surgery, Hanyang University College of Medicine, Seoul, Korea.

Correspondence to: Tai-Seung Kim, M.D. Department of Orthopaedic Surgery, Hanyang University College of Medicine, 17, Haengdang-dong, Seongdong-gu, Seoul 133-792, Korea. TEL: +82-2-2290-8481 or 8485, FAX: +82-2-2299-3774, kimts@hanyang.ac.kr

Received 8 October 2010 Accepted 9 January 2011

(open-access):

"This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited."

Abstract

Developmental coxa vara is a rare disease and the symptoms do not appear at birth, but rather, they appear at the age of walking. Clinically, the symptoms include a waddling gait, limb length discrepancy and frequent weariness. Developmental coxa vara is sometimes associated with skeletal dysplasia. Especially, it is associated with spondylometaphyseal dysplsia and the vertebral bodies and long bones are affected. The authors report here on diagnosing and treating this rare disease and we review the relevant literatures.

Keywords: coxa vara, spondylometaphyseal dysplasia, corner fracture

Figures and Tables

Figure 1

(A) A radiograph shows coxa vara with decreased neck-shaft angle and increased Hilgenreiner-epiphyseal angle (H-E angle). (B) A radio graph shows spondylometaphyseal dysplasia characterized with platyspondyly. (C) There is a marked sclerosis, flaring of the metaphyseal end of distal tibia and fibula. (D) Irregular areas of metaphyses also present corner fracture on medial aspect of proximal tibia.

Figure 2

Anteroposterior radiograph after subtrochanteric valgus osteotomy.

Figure 3

Anteroposterior radiograph taken 2 years after subtrochanteric valgus osteotomy shows the recurrence of developmental coxa vara on the right hip.

Figure 4

Anteroposterior radiograph after revision subtrochanteric valgus osteotomy due to recurrence of coxa vara.

Figure 5

This radiograph shows the decreased Hilgenreiner-epiphyseal angle 3 years after revision subtrochanteric valgus osteotomy.

References

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