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Moon, Yang, Yoon, Jang, Seo, Lee, and Choi: Jejunal Mesenteric Fibromatosis
Case Report
Journal of the Korean Surgical Society

Journal of the Korean Surgical Society 2010; 78(5): 320-324.

Published online: 10 May 2010

DOI: https://doi.org/10.4174/jkss.2010.78.5.320

Jejunal Mesenteric Fibromatosis

Hyung Hwan Moon, M.D.2, Song I Yang, M.D., Ki Young Yoon, M.D., Hui Kyoung Jang, M.D.1, Kyoung Won Seo, M.D., Sang Ho Lee, M.D., Kyoung Hyun Choi, M.D.3

Department of Surgery, Kosin University College of Medicine, Busan, Korea.

1Department of Pathology, Kosin University College of Medicine, Busan, Korea.

2Dongeui Medical Center, Busan, Korea.

3Department of Surgery, Haeundae Paik Hospital, Inje University, Busan, Korea.

Corresponding author (yoonky@ns.kosinmed.or.kr)

Received 22 September 2009       Accepted 18 November 2009

Copyright © 2010 The Korean Surgical Society

Abstract

Mesenteric fibromatosis is a rare benign fibrous tumor that can occur from bowel mesentery of the retroperitoneum. It can infiltrate the surrounding structures and tends to recur locally even after resection but does not have metastatic capability. Mesenteric fibromatosis represents 8% of all intra-abdominal desmoid neoplasm. We experienced a case of mesenteric fibromatosis in a 50-year-old woman with a painless abdominal mass. An exploratory laparotomy was performed, and two large, small bowel mesenteric masses were found which were invading the transverse colon. The segment of the jejunum and transverse colon including the masses were resected widely and the pathologic report confirmed the diagnosis of fibromatosis. We reviewed the features of the mesenteric fibromatosis, that is, clinical, imaging, pathological, immunohistological features, and differential diagnosis and treatment of mesenteric fibromatosis.

Keywords: Mesenteric fibromatosis, Desmoid tumor

Figures and Tables

Fig. 1
Abdominal CT finding. 7×8 cm sized low-attenuating mass is visible in the small bowel mesentery. The anterior small bowel is pressured by the mass.
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Fig. 2
Gross pathologic finding. Two retroperitoneal masses (10×9×4 cm, 7×7×3 cm) are noted on the serosal surface of small bowel. The cut surfaces of the masses are grayish white and firm with hemorrhage and myxoid apprearance.
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Fig. 3
Micro pathologic finding. These are composed of broad, sweeping fascicles of monotonous spindle cell with abundant collagenous stroma.
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Fig. 4
Immunohistochemical finding. Spindle cells show strong positivity for vimentin (A) and some nuclear staining for β-catenin (B).
jkss-78-320-g004

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