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Park: Pancreatoblastoma in Children
Case Report
Journal of the Korean Surgical Society

Journal of the Korean Surgical Society 2009; 77(Suppl): S29-S32.

Published online: 7 December 2009

DOI: https://doi.org/10.4174/jkss.2009.77.Suppl.S29

Pancreatoblastoma in Children

Jinyoung Park, M.D.

Department of Surgery, Kyungpook National University School of Medicine, Daegu, Korea.

Corresponding author (kpnugs@yahoo.co.kr)

Received 7 June 2009       Accepted 24 June 2009

Copyright © 2009 The Korean Surgical Society

Abstract

Pancreatoblastoma is a rare pediatric neoplasm with distinct acinar and squamoid differentiation that generally affects infants and young children. Although the prognosis is relatively favorable over typical pancreatic cancer, the optimal treatment of pancreatoblastoma has not been established. We experienced two cases of pancreatoblastoma in a 2-year-old girl and boy which was found incidentally by the parents due to the detection of abdominal masses.

Keywords: Pancreatoblastoma, Children

Figures and Tables

Fig. 1
Contrast enhanced abdominal computed tomography (CT) scan shows well-demarcated, inhomogenous mass with some calcification in head of pancreas.
jkss-77-S29-g001
Fig. 2
Cut surface of tumor shows yellowish area intermixing with myxoid area and focal cystic change. Mass is separated by fibrous septa.
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Fig. 3
Contrast enhanced abdominal CT scan shows well-defined solid mass, which is multilobulated by enhancing septa.
jkss-77-S29-g003
Fig. 4
Operative finding shows huge mass originating from tail of pancreas.
jkss-77-S29-g004
Fig. 5
Histological examination shows a distinct organoid pattern containing globular structures with elongated cells (Squamoid corpuscles: black arrow) and acinar cells (H&E stain, ×400).
jkss-77-S29-g005

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