Dermatofibrosarcoma in the Orbit: A Case Report

Dong Kyu Lee; Ga Eon Kim; Won Choi; Kyung Chul Yoon

doi:10.3341/JKOS.2016.57.11.1777

Journal List > J Korean Ophthalmol Soc > v.57(11) > 1010457

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Lee, Kim, Choi, and Yoon: Dermatofibrosarcoma in the Orbit: A Case Report

Case Report

J Korean Ophthalmol Soc 2016;57(11):1777-1780.

Published online: 25 September 2016

DOI: https://doi.org/10.3341/JKOS.2016.57.11.1777

Dermatofibrosarcoma in the Orbit: A Case Report

Dong Kyu Lee, MD¹, Ga Eon Kim, MD, PhD², Won Choi, MD, PhD¹, Kyung Chul Yoon, MD, PhD¹

¹Department of Ophthalmology, Chonnam National University Medical School, Gwangju, Korea

²Department of Pathology, Chonnam National University Medical School, Gwangju, Korea

Address reprint requests to Won Choi, MD, PhD Department of Ophthalmology, Chonnam National University Hospital, #42 Jebong-ro, Dong-gu, Gwangju 61469, Korea Tel: 82-62-220-6753, Fax: 82-62-227-1642 E-mail: wchoi82@hanmail.net

Received 11 August 2016 Revised 27 August 2016 Accepted 19 October 2016

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Purpose

Dermatofibrosarcoma in the orbit is a rare malignant neoplasm. We report an extremely rare case of primary dermatofibrosarcoma in the orbit.

Case summary

A 66-year-old male presented with a slowly progressing periorbital mass on his left upper eyelid which developed 3 weeks earlier. On physical examinations, a palpable firm mass under the skin was observed at the superomedial aspect of the left upper eyelid. However, there was no surface nodule or demarcated line on the eyelid. An approximately 1.2 × 1 × 1 cm sized well defined and clearly demancated mass was observed on orbital computed tomography. Excisional biopsy was performed under local anesthesia and pathological examination revealed dermatofibrosarcoma. There was no metabolic evidence of regional or distant metastasis based on positron emission tomography-computed tomography. Nine months after surgical excision there was no evidence of local recurrence.

Conclusions

This is the first report in South Korea of dermatofibrosarcoma in the orbit. Dermatofibrosarcoma should be considered following differential diagnosis of a periorbital mass.

Keywords: Dermatofibrosarcoma, Orbital mass

References

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Figure 1.

Clinical photos and Orbital computed tomography. Photograph of (A) 66-year-old man with a palpable firm mass under the skin at the superomedial aspect of the left upper eyelid. (B) Orbital computed tomography showed 1.2 × 1 × 1 cm sized well demarcated enhancing mass. (C) The orbital mass immediate after surgical excision. (D) The 9 months after operation showed no evidence of recurrence.

Figure 2.

Photographs of Histopathology. (A) Photograph of dermatofibrosarcoma by hematoxylin-eosin (×200). The tumor is composed of spindle cells with a fascicular arrangement. A mitotic activity is also shown. (B) Immunohistochemical staining shows CD34 positive cells (×200).

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