Journal List > J Korean Ophthalmol Soc > v.51(3) > 1008772

Song and Park: Bilateral Serous Retinal Detachment Associated With Alport's Syndrome

Abstract

Purpose

To report a case of bilateral serous retinal detachment associated with Alport's syndrome that resolved following intensive blood pressure control and electrolyte imbalance correction.

Case summary

A 50-year-old male patient presented with bilateral lenticonus and bilateral serous retinal detachment. Bilateral serous retinal detachment with retinal flecks characteristic of Alport's syndrome appeared along with the development of chronic renal failure and hypertension. The following kidney biopsy revealed Alport's syndrome. After 14 days, the serous detachment resolved and vision recovered following intensive blood pressure control and electrolyte imbalance correction fundus and FA results were nearly normal.

Conclusions

In this case, bilateral serous retinal detachment in Alport's syndrome resolved with intensive blood pressure control and electrolyte imbalance correction. To the author's knowledge, this is the first case in South Korea with documentation of the onset and resolution of bilateral serous retinal detachment in Alport's syndrome.

References

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Figure 1.
Bilateral anterior lenticonus was shown on slit-lamp examination.
jkos-51-463f1.tif
Figure 2.
The typical pictures of a drop of oil in water “oil-globule”.
jkos-51-463f2.tif
Figure 3.
Bilateral perimacular flecks with serous retinal detachment were shown.
jkos-51-463f3.tif
Figure 4.
Bilateral serous retinal detachment was found on OCT.
jkos-51-463f4.tif
Figure 5.
The following kidney biopsy revealed it to be Alport's syndrome; Stars indicate, from above, diffuse foot process effacement, compressed glomerular capillary lumina and GBMs increased in thickness and irregular wrinkled contours, respectively.
jkos-51-463f5.tif
Figure 6.
The serous retinal detachment resolved and the vision recovered following intensive blood pressure control and electrolyte imbalance correction.
jkos-51-463f6.tif
Figure 7.
Fluorescein angiogram findings were nearly normal after the serous retinal detachment resolved.
jkos-51-463f7.tif
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