A Case of Retinal Detachment Surgery in Albinism Patient

Ji-Wook Yang; Seung-Jin Lee; Seung-Bum Kang; Young-Hoon Park

doi:10.3341/jkos.2008.49.5.840

Journal List > J Korean Ophthalmol Soc > v.49(5) > 1008276

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Yang, Lee, Kang, and Park: A Case of Retinal Detachment Surgery in Albinism Patient

Original Article

J Korean Ophthalmol Soc 2008;49(5):840-844.

Published online: 7 September 2008

DOI: https://doi.org/10.3341/jkos.2008.49.5.840

A Case of Retinal Detachment Surgery in Albinism Patient

Ji-Wook Yang, M.D., Seung-Jin Lee, M.D., Seung-Bum Kang, M.D., Young-Hoon Park, M.D.

Department of Ophthalmology and Visual science, The Catholic University of Korea, Uijeongbu St. Mary's Hospital, Gyeonggi-do, Korea

Address reprint requests to Young-Hoon Park, M.D. Department of Ophthalmology, Uijeongbu St. Mary's Hospital, The Catholic University of Korea #65-1 Geumo-dong, Uijeongbu City, Gyeonggi 480-130, Korea Tel: 82-31-820-3110, Fax: 82-31-847-3418, E-mail: parkyh@catholic.ac.kr

Received 27 September 2007 Accepted 18 December 2007

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Purpose

To report a case of retinal detachment surgery in a patient with oculocutaneous albinism.

Case summary

A 44-year-old man visited our clinic complaining of decreased visual acuity in his left eye. His best corrected visual acuity was hand movement in his left eye, and rhegmatogenous retinal detachment involving the macula at the superior temporal site was found. We performed pars plana vitrectomy and attempted to reattach the retina using endolaser photocoagulation; however, the laser burn was not made, and we failed to reattach the retina. At that point, we carried out cryopexy around the retinal tear, and injected silicone oil into the vitreous cavity. Ten months after surgery, his best corrected visual acuity was 0.06, and there was no recurrent retinal detachment or proliferative vitreoretinopathy.

Conclusions

In patients with albinism with melanin deficiency, cryopexy is more useful than laser photocoagulation for retinal detachment surgery.

Keywords: Albinism, Cryopexy, Retinal detachment

References

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Figure 1.

A 44-year-old man with oculocutaneous albinism. (A) The photogram of the right eye shows hypopigmented skin, eyelash, and iris. Note the visible intraocular IOL optic and haptics through the hypopigmented iris. (B) Fluorescein angiogram shows early faded-out dye in the retinal vessels and visible choroidal vessels through the window-defect. (C) B-scan sonogram of the left eye showed bullous retinal detachment. (D) Light microcopy from the skin at the trunk shows generalized absence of melanin pigment (HE stain, ×200).

Figure 2.

The composite fundus photograms of a 44-year-old man with oculocutaneous albinism. (A) The fundus photograph of the right eye shows hypoplastic fovea and visible choroidal vasculature. (B) The fundus photograph of the left eye 6 months after retinal detachement operation shows well attached retina.

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