Abstract
Henoch-Schönlein purpura (HSP) is systemic vasculitis disease with various clinical manifestations. Gastrointestinal symptoms in patients with HSP are usually common, with an incidence rate of 62-90%. Most of these gastrointestinal symptoms occur after typical skin purpura, which is a very important clinical evidence for making a diagnosis of HSP. It is difficult to diagnose HSP without skin rash. About 25% of patients may experience gastrointestinal symptoms as their first symptoms. Herein, we report a case of ileo-colic intussusception associated with HSP in a 5-years-old girl presented with diffuse abdominal distension. Our patient did present any symptoms of HSP, such as purpura, arthralgia or arthritis, before surgery.
Figures and Tables
Fig. 1
Abominopelvic X-ray findings. (A) Supine simple abdomen showing dilated loops of the small intestine and bowel edema. (B) Erect simple abdomen showing multiple air-fluid levels with a step ladder sign.
![kjg-69-372-g001](/upload/SynapseData/ArticleImage/0028kjg/kjg-69-372-g001.jpg)
Fig. 2
Abdominopelvic computed tomography finding. Coronary view showing severe dilated small intestine and ileo-colic intussusception with target sign (arrow).
![kjg-69-372-g002](/upload/SynapseData/ArticleImage/0028kjg/kjg-69-372-g002.jpg)
Fig. 3
Operative findings. (A) Before manual reduction. The ileocolic type intussusception is observed (arrow). (B) After manual reduction. Severe hemorrhagic infarction in the small intestine is observed (arrow).
![kjg-69-372-g003](/upload/SynapseData/ArticleImage/0028kjg/kjg-69-372-g003.jpg)
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