Caroli Syndrome with Autosomal Recessive Polycystic Kidney Disease

Jae Sung Ko

doi:10.4166/kjg.2011.57.1.51

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Ko: Caroli Syndrome with Autosomal Recessive Polycystic Kidney Disease

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Korean J Gastroenterol 2011;57(1):51-53.

Published online: 4 October 2011

DOI: https://doi.org/10.4166/kjg.2011.57.1.51

Caroli Syndrome with Autosomal Recessive Polycystic Kidney Disease

Jae Sung Ko

Deparment of Pediatrics, Seoul National University College of Medicine, Seoul, Korea

Correspondence to: Jae Sung Ko, Deparment of Pediatrics, Seoul National University College of Medicine, 28, Yeongun-dong, Jongno-gu, Seoul 110-744, Korea. Tel: +82-2-2072-2197, Fax: +82-2-743-3455, E-mail: kojs@snu.ac.kr

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

References

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Fig. 1.

(A) A transverse ultrasonography of the liver showed coarse echogenicity of the liver parenchyme and mild intrahepatic duct dilatation (arrows). (B) Longitudinal ultrasonography showed enlarged kidney with increased echogenicity resulting from the multiple acoustic interfaces of the cysts.

Fig. 2.

Dilataion of the intrahepatic and extrahepatic bile ducts was demonstrated on MRCP (A). Note the multiple cysts in the kidneys on coronal T2 HASTE image (arrows, B).

Fig. 3.

Histology of liver showed diffuse periportal fibrosis, some cystically dilated bile ducts containing bile plugs, and bile ductular proliferation (H&E stain, ×200).

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