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Abstract
Protein C is an important physiological anticoagulant factor. Protein C deficiency has been linked to venous thrombosis at unusual sites, including the cerebral and mesenteric veins. Hereditary protein C deficiency is in-herited primarily as an autosomal dominant trait with incomplete penetrance. Protein C and S deficiencies are known to increase the risk of venous thrombosis and pulmonary thromboembolism. Testing for protein C levels and function is necessary for the detection of both type I and type II protein C deficiency. In this article, we report a case of pulmonary embolism and mesentery ischemia due to type 1 protein C deficiency.
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Fig. 1.
(A) Computed tomogram of abdomen showed dilatation of sigmoid colon associated with per-icolic fatty stranding (arrow) and small amount of fluid collection. (B) Surface rendering reconstruction image of abdomen showed no evidence of mesenteric artery occlusion.
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