A Case of Recurrent Bowel Perforation in a Patient with Churg-Strauss Syndrome

Chang Hoon Lee; Jeong Hoon Song; Sung Jo Jang; Yong Jae Han; Myeung Su Lee

doi:10.4078/jkra.2010.17.9.326

Journal List > J Korean Rheum Assoc > v.17(3) > 1003747

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Lee, Song, Jang, Han, and Lee: A Case of Recurrent Bowel Perforation in a Patient with Churg-Strauss Syndrome

Original Article

J Korean Rheum Assoc 2010;17(3):326-330.

Published online: 23 September 2010

DOI: https://doi.org/10.4078/jkra.2010.17.9.326

A Case of Recurrent Bowel Perforation in a Patient with Churg-Strauss Syndrome

Chang Hoon Lee¹, Jeong Hoon Song², Sung Jo Jang³, Yong Jae Han⁴, Myeung Su Lee¹

¹Departments of Internal Medicine, College of Medicine, Wonkwang University, Iksan, Korea

²Departments of Plastic Surgery, College of Medicine, Wonkwang University, Iksan, Korea

³Departments of Neurosurgery, College of Medicine, Wonkwang University, Iksan, Korea

⁴Department of Emergency Medicine, Wonkwang University Sanbon Hospital, Gunpo, Korea

Received 26 June 20102 August 2010 Accepted 2 August 2010

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Churg-Strauss syndrome is a rare systemic disorder characterized by asthma, eosionphilia and necrotizing vasculitis affecting small-to-medium-sized vessels. Although it is frequently associated with gastrointestinal mucosal lesions, recurrent bowel perforation is rare and potentially life threatening. We report a case of a 66-year-old man with Churg-Strauss syndrome, who presented with recurrent small bowel perforation. He was admitted with abdominal pain developed previous night, who had a previous small bowel perforation history treated with laparoscopic closure 5 months ago. Laboratory data showed remarkable eosinophilia. Physical examination indicated positive signs of peritoneal irritation in the entire abdomen, and abdominal computed tomography scanning showed edematous small bowel with intra-abdominal free air, suggesting intestinal perforation. He underwent laparoscopic small bowel closure and was treated with steroid.

Keywords: Churg-Strauss syndrome, Recurrent bowel perforation, Laparoscopic closure, Steroid

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Fig. 1.

Chest radiography shows bilateral patchy consolidation and increased interstitial marking of left lower lung field with bihilar nodular lesion.

Fig. 2.

Abdominal computed tomography image shows intra-abdominal free-air (arrow) indicating bowel perforation.

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