Abstract
Cogan's syndrome can accompany a variety of systemic vasculitides including aortitis. A 45-year-old woman with a history of typical Cogan's syndrome presented with orthopnea and exertional dyspnea. Echocardiography demonstrated severe aortic valve insufficiency. Computed tomographic angiography demonstrated active vasculitis affecting the ascending and descending aortas and also showed stenosis of the left subclavian artery, both renal arteries, the celiac axis, the superior mesenteric artery, and the right common iliac artery. She received high dose corticosteroid and then underwent an aortic valve replacement. This is the first case of Cogan's syndrome with aortitis in Korea.
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Fig. 1.
Initial axial views of computed tomographic angiography revealed a thickened vascular wall with delayed enhancement in the right carotid artery, aortic arch, and descending aorta (A). The 3-D reconstruction images showed focal or diffuse stenotic lesions of the major branches of the aortic arch and abdominal aorta (B). Black thick arrow, the left common carotid artery; black thin arrow, the right innominate artery and common carotid artery; white thick arrow, the left subclavian artery; white thin arrow, the right common iliac artery.
![jkra-17-301f1.tif](/upload/SynapseXML/0010jkra/thumb/jkra-17-301f1.gif)