A Case of Systemic Lupus Erythematosus and Abdominal Aorta Thrombosis Associated with Protein C and S Deficiency

Jun Ho Song; Tae Geun Gweon; Jun Ki Min

doi:10.4078/jkra.2009.16.4.306

Journal List > J Korean Rheum Assoc > v.16(4) > 1003690

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Song, Gweon, and Min: A Case of Systemic Lupus Erythematosus and Abdominal Aorta Thrombosis Associated with Protein C and S Deficiency

Original Article

J Korean Rheum Assoc 2009;16(4):306-311.

Published online: 20 January 2009

DOI: https://doi.org/10.4078/jkra.2009.16.4.306

A Case of Systemic Lupus Erythematosus and Abdominal Aorta Thrombosis Associated with Protein C and S Deficiency

Jun Ho Song, Tae Geun Gweon, Jun Ki Min

Division of Rheumatology, Department of Internal Medicine, College of Medicine, The Catholic University of Korea, Seoul, Korea

Received 21 May 2009 Revised 11 August 2009 Accepted 17 August 2009

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Thrombosis is a well known manifestation in patients with systemic lupus erythematosus, along with lupus anticoagulant, anticardiolipin antibody and anti β2-glycoprotein I. We describe here a 44-year-old female with an abdominal aorta thrombosis of SLE and the patient had no antiphospholipid antibodies. She had this unusual site of thrombosis and this was associated with protein C and S deficiency. She had no other cause of thrombosis. After anticoagulant treatment, her thrombosis of the abdominal aorta resolved.

Keywords: Systemic lupus erythematosus, Thrombosis, Aorta, Protein C and S deficiency

References

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Fig. 1.

(A) This picture shows peripheral cyanosis of the fingers. (B) This picture shows splinter hemorrhages on the finger nail.

Fig. 2.

Abdominal CT revealed target-appearing concentric wall thickening and mesenteric edema in the proximal jejunum at the time of admission.

Fig. 3.

(A) Abdominal computed tomography revealed a thrombosis on the abdominal aorta. (B) Abdominal ultrasonography revealed a thrombosis in the abdominal aorta at that time.

Fig. 4.

There is no thrombosis in the abdominal aorta after anticoagulation treatment.

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