Journal List > J Korean Rheum Assoc > v.14(2) > 1003558

Woo, Chang, and Yoo: A Case of Pulmonary Hypertension in a Patient with Adult-onset Still's Disease

Abstract

Pulmonary hypertension is one of the serious complications of autoimmune rheumatic disease, and it is becoming an important cause of morbidity and premature death. Pulmonary involvement occurs occasionally in adult-onset Still's disease (AOSD), but pulmonary hypertension has not been previously reported in Korea. We describe a 33-year-old woman with 5-year history of AOSD who presented with pulmonary hypertension, without evidences of pleural or parenchymal involvement of the lung, pulmonary embolism or any other obvious cause. Here, we report an AOSD patient with pulmonary hypertension with review of the literatures.

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Fig. 1.
Chest PA shows enlarged central pulmonary arteries.
jkra-14-176f1.tif
Fig. 2.
Transthorasic echocardiography shows D-shape left ventricular cavity.
jkra-14-176f2.tif
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